Bone change in intermediate β-thalassemia
Abstract
Intermediate β-thalassemia is a moderate clinical condition between small thalassemia and large thalassemia. These patients do not need regular blood transfusions throughout their lives, although they may need blood transfusions under certain clinical conditions and usually over a period of time (surgery, pregnancy, infection). Intermediate thalassemia has a wide clinical spectrum, from a form with moderate anemia (hemoglobin level of 70-100 g / l) to a condition with more severe anemia, which manifests itself in the first 2-6 years of life. Since these patients usually do not require routine transfusions, as mentioned above, intermediate thalassemia is classified as transfusion-independent thalassemia [1-3]. These patients, as well as patients with large thalassemia, require careful attention of a clinician to improve the quality of life [4-7].
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Keywords
bone changes
osteoporosis промежуточная β-талассемия
изменения в костях
остеопороз aralıq β-talassemiya
sümük dəyişiklikləri
osteoporoz
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